Moyamoya Syndrome with Primary Antiphospholipid Syndrome

Moyamoya syndrome with primary antiphospholipid syndrome.

OBJECTIVES To report a rare case of moyamoya syndrome with primary antiphospholipid syndrome (APS). CLINICAL PRESENTATION AND INTERVENTION A 41-year-old woman was admitted with sudden onset of left-sided hemiparesis. Magnetic resonance imaging and magnetic resonance angiography of the brain showed characteristic features of moyamoya vessels. Laboratory investigations revealed raised levels of...

Catastrophic Primary Antiphospholipid Syndrome

drome (APLS) may present with a catastrophic condition characterized by multiple vascular occlusions that often result in death if appropriate treatment is not quickly applied. In the great majority of cases, patients with catastrophic APLS show a spontaneous tendency to develop microvascular thrombosis that affects multiple organs. However, arterial reactivity leading to acute thrombosis after...

Severe primary antiphospholipid syndrome.

Antiphospholipid syndrome (APS) is characterised by recurrent venous or arterial thrombosis and/or fetal losses. In APS, the homeostatic regulation of blood coagulation is altered, however, the mechanism of thrombosis is not yet defined and it has varied manifestations. Deep vein thrombosis with or without pulmonary embolism is the most common manifestation followed by arterial occlusion of cer...

Primary antiphospholipid syndrome presenting with homonymous quadrantanopsia

Purpose To report a case of primary antiphospholipid syndrome presenting with isolated homonymous superior quadrantanopsia. Observations A 50-year-old Korean man presented with subjective visual disturbance for 1 month. Visual field testing showed a right homonymous superior quadrantanopsia. Brain magnetic resonance imaging (MRI) revealed an old infarct in his left occipital lobe and multiple...

Antiphospholipid Syndrome Presenting with Superior Vena Cava Thrombosis